Cystic fibrosis and liver disease
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چکیده
As the mean age of survival for patients with cystic fibrosis (CF) continues to improve, the diagnosis and treatment of CF liver disease (CFLD) has become a very relevant clinical issue. Cystic fibrosis liver disease is the third most frequent cause of death in CF after respiratory and transplantation complications and accounts for 2.3% of all mortality (Cystic Fibrosis Foundation, 2002). Liver disease is the initial diagnostic finding in 1.5% of patients, suggesting that all patients with unexplained cirrhosis should have a sweat test as part of their diagnostic evaluation (Collardeau-Frachon et al, 2007).
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تاریخ انتشار 2009